Encephalitis

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Encephalitis:

Encephalitis Dr Rahul Chakor Lecturer – Neurology T. N. Medical. College B. Y. L. Nair Hospital Mumbai

Encephalitis:

Encephalitis Inflammation of the cerebral parenchyma, meninges – Meningoencephalitis Gray Matter, White matter, Gray – white junction, gray matter nuclei, brainstem

Encephalitis:

Encephalitis Blood borne Retrograde neuro-axonal Neuronal receptors

Encephalitis:

Encephalitis Numerous viruses Infective microorganisms - bacteria, fungii, parasites Drugs (NSAIDs) Autoimmune disorders - SLE, vasculitis Postinfective - ADEM

Viral Encephalitis:

Viral Encephalitis Herpesviruses HSV 1 and 2 Varicella zoster CMV Arboviruses Japanese virus Eastern equine virus Western equine virus West Nile Enteroviruses Coxackie Echo Adenoviruses HIV Measles Mumps Rabies Nippah

Encephalitis:

Encephalitis Bacterial TB Listeria Whipple disease Rickettsia Syphilis Lyme

Etiology:

Etiology Fungi Cryptococcosis Parasites Toxoplasmosis Malaria Cysticercosis Paraneoplastic Limbic, brainstem

Herpes Encephalitis:

Herpes Encephalitis HSV 1 (oral mucosa) – a common cause HSV 2 (genital infection) – neonatal Most common cause of sporadic viral encephalitis

Herpes Encephalitis:

Herpes Encephalitis Pathogenesis - Virus latent in trigeminal ganglia, reactivated and spreads along olfactory tract - Virus spreads along nerve fibers innervating meninges of anterior and middle fossae

Herpes Encephalitis:

Herpes Encephalitis Pathology Intense inflammation, necrosis, ( necrotizing encephalitis ) Hemorrhagic lesions in the medial temporal lobes, medial frontal and orbitofrontal regions, Cingulate gyrus, Insular cortex, lateral temporal lobes, midbrain, pons

Symptoms:

Symptoms Evolve over several days or acutely Fever, headache, confusion, stupor, coma (temporal lobe swelling & uncal herniation) Seizures, status epilepticus Psychotic behavior, personality changes, irritability delirium Temporal lobe seizures - Gustatory or olfactory hallucinations, anosmia

Diagnosis:

Diagnosis CSF Increased pressure, pleocytosis (10 – 500 cells/mm 3 ) lymphocytes, normal initially, RBCs, xanthocromia, raised proteins, normal glucose, HSV antigen, DNA, detection by PCR

Diagnosis:

Diagnosis Neuroimaging CT scan – Hypodensity in 50 – 60 % of cases MRI – Increased T2 signal in > 90% cases Contrast enhancement

Slide 14:

Herpes Encephalitis

Slide 15:

MRI – Herpes Encephalitis

EEG:

EEG PLEDs

Slide 17:

Pathology

Differential diagnosis :

Differential diagnosis ADEM Cerebral venous thrombosis Subdural Empyma Cerebral Abscess Septic Embolism

Treatment:

Treatment General Medical Care Increased ICP – Head elevation, diuretic, steroids, mannitol, hyperventilation Seizures – Phenytoin, Carbamazepine, Benzodiazepine

Treatment:

IV Acyclovir 10mg/kg tid for 14 days in any proven or suspected case of Herpes Encephalitis Adverse effects – IV irritation, renal dysfunction Treatment

Treatment:

Outcome Depends on age and level of consciousness Survival more than 90% when treatment begun within 4 days of onset in conscious patient Squelae – Dementia, temporal lobe epilepsy, Korsakoff amnesic syndrome Treatment

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