Sarcoidosis 3

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Pulmonary Sarcoidosis: 

Pulmonary Sarcoidosis Yogin Patel Radiology Elective April 6th 2004

Agenda: 

Agenda Clinical presentation Evaluation Radiographic Findings Discussion

Clinical Presentation: 

Clinical Presentation History 24 YO AA M with 2 weeks of pleuritic chest pain Other Symptoms Fever, anorexia, arthralgias, DOE, cough, hemoptysis Physical Exam Neuro: CN palsy Optho: Uveitis Card: Cardiomyopathy, pericarditis GI: Hepatic granulomas, cholestasis Lungs: Restriction Renal: Nephrolithiasis Derm: Erythematous nodules Heme: Anemia, thrombocytopenia, leukopenia

Radiographic Findings: 

Radiographic Findings

Evaluation: 

Evaluation Routine labs – Primarily useless Lab abnormalities associated with areas of involvement (↑ Alk Phos with hepatic involvement) Kveim Test Angiotensin Converting Enzyme elevation ACE is secreted by granulomas and may be present in serum, CSF, BAL washings Biopsy Noncaseating granulomas

Radiographic Findings: 

Radiographic Findings

Radiographic Findings: 

Radiographic Findings

Radiographic Findings: 

Radiographic Findings

Pulmonary Sarcoidosis: 

Pulmonary Sarcoidosis

Treatment: 

Treatment Treat? Symptomatic Therapy NSAIDS Corticosteroid Therapy Prednisone Non-steroid Therapy Methotrexate Hydroxychloroquinine

References: 

References Shorr, Andrew. “Sarcoidosis”. eMedicine http://www.emedicine.com/MED/topic2063.htm Rockoff SD. “Unusual manifestations of thoracic sarcoidosis”. AJR 1985 144: 513-528 (Review article) Harris, Hugh and Priscilla Sarinas. “Sarcoidosis”. Best Practice of Medicine. June 2001. http://merck.praxis.md/index.asp?page=bpm_brief&article_id=BPM01PU06 Williams, Scott. Sarcoidosis. http://www.auntminnie.com/ScottWilliamsMD2/Chest/Autoimmune/Sarcoid/Sarcoid.htm