Sarcoidosis 3

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Pulmonary Sarcoidosis:Pulmonary Sarcoidosis Yogin Patel Radiology Elective April 6th 2004


Agenda:Agenda Clinical presentation Evaluation Radiographic Findings Discussion


Clinical Presentation:Clinical Presentation History 24 YO AA M with 2 weeks of pleuritic chest pain Other Symptoms Fever, anorexia, arthralgias, DOE, cough, hemoptysis Physical Exam Neuro: CN palsy Optho: Uveitis Card: Cardiomyopathy, pericarditis GI: Hepatic granulomas, cholestasis Lungs: Restriction Renal: Nephrolithiasis Derm: Erythematous nodules Heme: Anemia, thrombocytopenia, leukopenia


Radiographic Findings:Radiographic Findings


Evaluation:Evaluation Routine labs – Primarily useless Lab abnormalities associated with areas of involvement (↑ Alk Phos with hepatic involvement) Kveim Test Angiotensin Converting Enzyme elevation ACE is secreted by granulomas and may be present in serum, CSF, BAL washings Biopsy Noncaseating granulomas


Radiographic Findings:Radiographic Findings


Radiographic Findings:Radiographic Findings


Radiographic Findings:Radiographic Findings


Pulmonary Sarcoidosis:Pulmonary Sarcoidosis


Treatment:Treatment Treat? Symptomatic Therapy NSAIDS Corticosteroid Therapy Prednisone Non-steroid Therapy Methotrexate Hydroxychloroquinine


References:References Shorr, Andrew. “Sarcoidosis”. eMedicine http://www.emedicine.com/MED/topic2063.htm Rockoff SD. “Unusual manifestations of thoracic sarcoidosis”. AJR 1985 144: 513-528 (Review article) Harris, Hugh and Priscilla Sarinas. “Sarcoidosis”. Best Practice of Medicine. June 2001. http://merck.praxis.md/index.asp?page=bpm_brief&article_id=BPM01PU06 Williams, Scott. Sarcoidosis. http://www.auntminnie.com/ScottWilliamsMD2/Chest/Autoimmune/Sarcoid/Sarcoid.htm